Management of spinal deformity caused by a hemivertebra is controversial. Early diagnosis and early aggressive surgical treatment are mandatory in progressive cases. Several techniques have been reported for the surgical treatment of young children with congenital spinal deformities. There have been concerns regarding epidural bleeding, neurological complications, pedicle screw placement, implant failure and prominence of posterior constructs in this very young age group for posterior instrumented patients. A single partial corpectomy of the hemivertebra with anterior instrumentation and simultaneous posterior non-instrumented fusion can offer a new alternative which can avoid these concerns. Anterior instrumentation is safe and effective technique capable of transmitting a high amount of convex compression allowing short segment fusion which is of great importance in the growing spine, meanwhile allows control of segmental kyphosis.