Tetanus is a life- threatening nervous system disease caused by Clostridium tetani (C. tetani). It is characterized by an acute onset of hypertonia, painful muscular contractions (usually of the neck and jaw muscles), and generalized muscle spasms without other apparent medical causes. However, various atypical forms of clinical presentation were reported worldwide and need to be clarified. Being aware of these atypical presentations helps to achieve early diagnosis and management of this dreadful condition. Here, we emphasize different experience through many worldwide case reports about atypical presentation of tetanus.