Background: One of the most prevalent causes of shock and mortality in newborns is coarctation of the aorta (CoA). Because there are no audible murmurs and the blockage from the coarctation does not emerge for several days after birth, it may be the most difficult kind of serious congenital heart disease (CHD) to detect. Despite the ease of clinical diagnosis, pediatric patients often go undetected since they are often asymptomatic. Objective: This review aimed to highlight the key points and challenges in management of COA in pediatrics. Methods: We searched PubMed, Google Scholar, and Science Direct using the following keywords: Balloon dilatation, stent, coarctation of the aorta, and patent ductus arteriosus. The writers also assessed references from pertinent literature and they only included the most current or comprehensive study. Documents in languages other than English had not been included since there are insufficient sources available for translation. They excluded unpublished manuscripts, oral presentations, conference abstracts, and dissertations where they were not considered part of the scope of important scientific inquiries. Conclusion: The majority of coarctation falls into two categories: Critical CoA, which causes symptoms within two months of birth and if left untreated, results in mortality, and asymptomatic CoA, which appears later, generally with hypertension in the upper limbs. Critical CoA accounts for approximately 60% of all coarctation. Despite, improvements in medical care and management strategies, long-term survival has not altered much.