1.Introduction. - Ewing sarcoma is a tumour in children and young adults that usually starts in the bone. Extraskeletal Ewing
sarcoma is rare, and its cutaneous localization is exceptional. We report a new case of primary cutaneous Ewing sarcoma.
2.Observation. - A 22-year-old man was presented for a skin tumor on the scalp that had been evolving for six months. MRI
showed a tumor process of the left occipital region of the scalp without bony involvement of the cranial vault or endocranial
extension. The patient underwent a biopsy. Histopathological examination showed round mesenchymal cells expressing CD99.
The treatment was extended surgical excision, chemotherapy and radiotherapy.
3.Discussion. – Cutaneous Ewing sarcoma is a rare pathology, difficult to diagnose even from an anatomopathological point
of view. Confirmation of the diagnosis by molecular biology methods is therefore essential. Due to its rarity, there is little data
on specific treatment recommendations. Currently, cutaneous Ewing sarcomas are treated like bone Ewing sarcomas. The
prognosis, according to the data in the literature, is much more favorable than bone Ewing sarcomas.