Isolated pulmonary valve stenosis (PS) constitutes 7.5–9% of all congenital heart diseases. Percutaneous balloon pulmonary valvotomy (BPV) is the treatment of choice for the isolated PS. BPV is preferred in moderate-to-severe pulmonary stenosis and typical dome-shaped valvular PS. BPV is also the preferred treatment in neonates with critical pulmonary stenosis. BPV success rate is lesser with dysplastic valves. As a part of the team, an anesthesiologist not only helps in anesthesia management of the procedure but prompt management of the complications, especially during manipulation across RVOT, balloon inflation, and postoperative course.