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247042

Neonatal Biliary Obstruction Caused by Pancreatic Kaposi Hemangioendothelioma

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Last updated: 22 Jan 2023

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Abstract

Kaposiform hemangioendothelioma (KHE), is a rare benign locally invasive proliferation of blood vessels that forms a mass. Besides the mass effect of KHE, it infiltrates adjacent tissues, it can be associated with severe thrombocytopenia, consumptive coagulopathy with high mortality rate. The manifestations of KHE are variable and range from cutaneous lesions with wide varieties of appearances to deep masses without cutaneous signs. We report a case of 3 month old male who presented as extrahepatic biliary atresia in the form of jaundice, hepatomegaly, clay colored stool and elevated liver enzymes. Dynamic Magnetic Resonance Imaging revealed pancreatic head solid mass. Operative findings and biopsy of the highly vascular lesion confirmed  that it was KHE  of head of pancreas. The mass was excised and hepato-portoenterostomy was successfully performed. One year later the boy is disease free with no organomegaly or any other complication. KHE of head of pancreas is a very rare cause of extrahepatic biliary obstruction early in life. It is amenable to successful surgical intervention.

DOI

10.21608/cupsj.2022.141453.1056

Keywords

Pancreatic kaposiform hemangioendothelioma, extrahepatic biliary obstruction, hepato-portoenterostomy

Authors

First Name

Magd

Last Name

Kotb

MiddleName

-

Affiliation

Department of Pediatrics, Faculty of Medicine, Cairo University, Egypt

Email

magdkotb@kasralainy.edu.eg

City

cairo

Orcid

https://orcid.org/00

First Name

Sherif

Last Name

Kaddah

MiddleName

-

Affiliation

Department of Pediatric Surgery, Faculty of Medicine, Cairo University, Egypt

Email

skaddah@hotmail.com

City

-

Orcid

-

First Name

Sally

Last Name

El Sorogy

MiddleName

-

Affiliation

Department of Pediatrics, Public Mounira Hospital, Cairo, Egypt

Email

dr.sally194@gmail.com

City

cairo

Orcid

0000-0003-0666-0408

First Name

Reham

Last Name

Mahmoud

MiddleName

-

Affiliation

Department of Radiodiagnosis, Faculty of Medicine, Cairo University, Egypt

Email

reham_2006@hotmail.com

City

cairo

Orcid

0000-0001-9192-4089.

First Name

Naglaa

Last Name

El Kinaaiee

MiddleName

-

Affiliation

Department of Pathology, Cancer Institute, Cairo University, Egypt

Email

naglaa.elkinaai@gmail.com

City

cairo

Orcid

0000-0002-3752-3708

First Name

Sayed

Last Name

Khedr

MiddleName

-

Affiliation

Department of Pediatric Surgery, Faculty of Medicine, Cairo University, Egypt

Email

sayed_khedr@kasralainy.edu.eg

City

cairo

Orcid

-

First Name

Mostafa

Last Name

Gad

MiddleName

-

Affiliation

Department of Pediatric Surgery, Faculty of Medicine, Cairo University, Egypt

Email

mostafagad@kasralainy.edu.eg

City

cairo

Orcid

-

Volume

2

Article Issue

2

Related Issue

35212

Issue Date

2022-07-01

Receive Date

2022-05-29

Publish Date

2022-07-01

Page Start

210

Page End

215

Print ISSN

2805-279X

Online ISSN

2682-3985

Article File

CUPSJ_Volume 2_Issue 2_Pages 210-215.pdf

PDF . 878.1kB

Link

https://cupsj.journals.ekb.eg/article_247042.html

Detail API

https://cupsj.journals.ekb.eg/service?article_code=247042

Order

12

Type

Case Report

Type Code

1,279

Publication Type

Journal

Publication Title

Pediatric Sciences Journal

Publication Link

https://cupsj.journals.ekb.eg/

MainTitle

-

Details

Type

Article

Created At

22 Jan 2023