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179788

Unusual Presentation of Atypical Kawasaki Disease in a Child with Thrombocytopenia and Spontaneous Femoral Artery Leak: A Case Report

Article

Last updated: 04 Jan 2025

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Abstract

Kawasaki disease (KD) is an acute systemic vascular disease that affects mostly medium sized and small vessels. The most serious of which is coronary artery disease. Vasculitis involves proliferative granulomatous inflammation and resolves by cicatrization if not treated. It is generally a self-limited disease and its highest incidence is in children under five years.  The diagnostic criteria include the presence of fever for at least 5 days along with four of five other clinical features (rash, mucositis, conjunctival injection, cervical lymphadenopathy or extremity changes). Atypical Kawasaki disease includes patients who meet only 2 or 3 of the 5 criteria for diagnosis. We here report a 4- year old male patient who presented with fever, mucositis, perineal rash and evidence of de novo femoral vasculitis leading to spontaneously leaking femoral arteritis. His complete blood count revealed thrombocytopenia. The patient fulfilled the criteria for the diagnosis of atypical Kawasaki Disease.  He received intravenous immunoglobulins and aspirin in anti-inflammatory doses and his condition improved. We report this unusual presentation of Kawasaki disease with spontaneous femoral artery leak, rash and thrombocytopenia. Diagnosis of atypical Kawasaki disease is very challenging but essential as initiation of specific management is life-saving.  

DOI

10.21608/cupsj.2021.61910.1013

Keywords

Atypical Kawasaki Disease, thrombocytopenia, extracoronary aneurysms, Femoral vasculitis, Perineal desquamation

Authors

First Name

Mohamed

Last Name

Eid

MiddleName

S.

Affiliation

Department of Pediatrics, Cairo University, Cairo, Egypt

Email

mohamed_samir_eid@cu.edu.eg

City

Giza

Orcid

0000-0003-4245-7482

First Name

Ahmed

Last Name

Badr

MiddleName

-

Affiliation

Department of Pediatrics, Cairo University, Cairo, Egypt

Email

abadr2007@yahoo.com

City

Giza

Orcid

-

First Name

Hala

Last Name

Hamza

MiddleName

S.

Affiliation

Department of Pediatrics, Cairo University, Cairo, Egypt

Email

dr.hala_hamza@hotmail.com

City

Cairo

Orcid

-

First Name

Yasser

Last Name

Sedky

MiddleName

-

Affiliation

Department of Pediatrics, Cairo University, Cairo, Egypt

Email

ymsedky@hotmail.com

City

Cairo

Orcid

-

Volume

1

Article Issue

2

Related Issue

25899

Issue Date

2021-07-01

Receive Date

2021-03-09

Publish Date

2021-07-01

Page Start

107

Page End

110

Print ISSN

2805-279X

Online ISSN

2682-3985

Article File

CUPSJ_Volume 1_Issue 2_Pages 107-110.pdf

PDF . 3.2MB

Link

https://cupsj.journals.ekb.eg/article_179788.html

Detail API

https://cupsj.journals.ekb.eg/service?article_code=179788

Order

7

Type

Case Report

Type Code

1,279

Publication Type

Journal

Publication Title

Pediatric Sciences Journal

Publication Link

https://cupsj.journals.ekb.eg/

MainTitle

Unusual Presentation of Atypical Kawasaki Disease in a Child with Thrombocytopenia and Spontaneous Femoral Artery Leak: A Case Report

Details

Type

Article

Created At

22 Jan 2023