Abstract:
Background: Ebstein's anomaly is an uncommon clinical syndrome accounting for approximately 0.5% of congenital heart disease(CHD) patients. It is defined as a congenital displacement of the posterior and septal leaflets of the tricuspid valve towards the right ventricular apex whichresults in atrialization of a part of the right ventricle. Aim andobjectives: Review the pathological spectrum of Ebstein´s Anomaly inadults, illustrate by MR the morphologic aspects of EA. Discuss MR Findings of right ventricular overload including right ventricular dimension, paradoxical ventricular septal motion.Emphasize the role of MR in the assessment of ventricular and valvular function. Demonstrate the use of delayed contrast-enhanced MR to rule out segments of myocardial dysplasia, Subjects and Methods: The present study involved twenty patients who were previously diagnosed for assessment and treatment of Ebstein anomaly . The clinical records and surgical details of all identified patients were examined, and Participants were selected from the outpatients in National Heart Institute, Giza, Egypt. Results: results of the study revealed that Ebstein`S anomaly severely affecting tricuspid regurge since 75% of patients (15 of 20) were affected while only one patient (5%) suffered of mild regurge and four patients (20%) suffered of moderate regurge, Conclusion: The diagnosis of Ebstein's anomaly is usually based on echo findings; however, cardiac magnetic resonance imaging(CMR) can add useful information enabling a detailed visualization of cardiac abnormality, as well as a method of accurate physiological evaluation. CMR, in conjunctionwith echocardiography,offers a comprehensive non-invasive evaluation either for surgical management or ongoing follow-up of these patients.