Group A Streptococcus commonly causes cellulitis and pharyngitis, but in rare instances, it may cause pneumonia. Herein, we report a case of invasive pneumonia with classic symptoms of Kawasaki disease (KD). This case highlights the importance of considering KD in patients with pneumonia, especially when they present with typical KD features and do not respond to antibiotics. Objectives: To present our case of invasive pneumonia with skin peeling caused by group a beta-hemolytic streptococcus and kawasaki disease presented to General Pediatric Unit, King Saud University Medical City, Riyadh, Saudi Arabia. Subjects and Methods: Case study of a four-years-old boy who was presented to the hospital with fever, cough, and dyspnea that persisted for 7 days. His medical history was unremarkable, and his immunizations were up to date as per the Saudi Ministry of Health vaccination schedule for children of that age. Results: As a result, the final diagnosis was confirmed as KD with GAS. Treatment with vancomycin and tazocin was sustained for a whole of three weeks, and subsequently the case was discharged after a follow-up cardiology examination. Echocardiography was repeated after six weeks of illness with no evidence of coronary dilatation. Conclusion: A diagnosis of KD should be considered in patients with pneumonia who exhibit the characteristic symptoms of KD, especially when a poor response to antibiotic treatment is observed.