Primary congenital glaucoma is an early onset developmental glaucoma (EODG) with unique features in its pathophysiology, clinical presentation and management. Intraocular pressure (IOP) measuring is tricky in both technique and interpretation of its values. Optic disc cupping plays a more central part in follow-up of EODG than in follow-up of adult glaucoma. Management of EODG is essentially surgical. Angle surgeries; trabeculotomy and goniotomy, have the highest success rates in literature. Both of these time-honored techniques have new developments to enhance their outcomes. Other conventional techniques that are successful in adults like trabeculectomy, non-penetrating surgery and
valve surgery show poorer results in infants.