We report a case of 50 years old male with neurofibromatosis complaining of recurrent attacks of right loin pain. Clinically , the patient was normotensive , his body was full of neurofibromas with cafe au lait patches (Fig. 1, 2 & 3). Catecholamine in urine was markedly elevated. No other endocrinological abnormality depicted. CT scan abdomen revealed presence of right adrenal mass 5.9X5.9 cm with central necrosis and haemorrage (Fig. 4 & 5). I 131 metaiodobenzylguanidine (I 131-MIBG) revealed a well defined sizable area of intense tracer accumulation at right suprarenal gland (fig. 6 & 7). The patient was operated upon and the histopathology proved to be benign pheochromocytoma.