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61444

The Clinical Impact of Delayed Management of Hirschsprungs Disease

Article

Last updated: 22 Jan 2023

Subjects

-

Tags

General Surgery

Abstract

Background: Hirschsprung's disease (HD) is a developmental disorder of the enteric nervous system that is characterized by the absence of ganglion cells in the myenteric and submucosal plexus from the anorectum for a variable colonic or intestinal distance. HD is a congenital bowel motility disorder which occurs in approximately one of every 5000 live births. This results in a lack of peristalsis leading to a huge dilatation of the colon proximal to the aganglionic bowel. Aim of work: The purpose of the present study is to investigate the clinical impact of delayed management of children with HD. and how it would affect their outcomes? Methods: The present study was performed in the period from July 2018 to august 2019 in Pediatric Surgery Department of Zagazig University Hospital. 18 patients enrolled inprospective clinical study Results: The delayed diagnosis of HD is associated with a different pattern of presentation compared with neonatal HD. Most of the cases were presented by chronic constipation, abdominal distension and bilious vomiting. Moreover, outcome is worse in older children who are diagnosed with this disease. Conclusions: HD in older children associated with long hospital stay, increased cost of treatment compared with the younger children. Postoperative outcome in older children associated not only with increased risk of serious morbidities but also indirectly affect their long-term outcome.

DOI

10.21608/zumj.2019.18040.1583

Keywords

Hirschsprung's disease, Aganglionic, outcomes

Authors

First Name

Emad

Last Name

Alshatti

MiddleName

Ali Ali

Affiliation

Department of General Surgery, Faculty of Medicine - Zawia University, Libya

Email

imadashatti88.com@gmail.com

City

-

Orcid

-

First Name

Khaled

Last Name

El Sayed Fahmi

MiddleName

Safwat

Affiliation

Department of General Surgery, Faculty of Medicine - Zagazig University, Egypt

Email

kh_safwat@yahoo.com

City

-

Orcid

-

First Name

Ali

Last Name

Elshewy

MiddleName

Helmy Abdelwahed

Affiliation

Department of General Surgery, Faculty of Medicine - Zagazig University, Egypt

Email

dr_ali_elshewy@yahoo.com

City

Mit Ghamr

Orcid

-

First Name

Ahmed

Last Name

Rozeik

MiddleName

Ezzat

Affiliation

Department of Pediatric Surgery, Faculty of Medicine - Zagazig University, Egypt

Email

ahmed_ezzat147@yahoo.com

City

-

Orcid

-

Volume

28

Article Issue

4

Related Issue

35321

Issue Date

2022-07-01

Receive Date

2019-10-10

Publish Date

2022-07-01

Page Start

653

Page End

658

Print ISSN

1110-1431

Online ISSN

2357-0717

Link

https://zumj.journals.ekb.eg/article_61444.html

Detail API

https://zumj.journals.ekb.eg/service?article_code=61444

Order

5

Type

Original Article

Type Code

273

Publication Type

Journal

Publication Title

Zagazig University Medical Journal

Publication Link

https://zumj.journals.ekb.eg/

MainTitle

-

Details

Type

Article

Created At

22 Jan 2023