Ameloblastoma is a benign odontogenic tumor most commonly occuring in the jaw bones. It develops from
the residual epithelium of the tooth germ, epithelium of odontogenic cysts stratified squamous
epithelium and epithelium of the enamel organ. About 80% of ameloblastomas occur in the
mandible mainly the molar - ramus region and the rest 20% in the maxilla. Ameloblastoma
clinically appears as an aggressive odontogenic tumor, often asymptomatic and slow-growing,
with no evidence of swelling which affects the treatment outcome. Since ameloblastoma is
also associated with a high rate of recurrence when treated inadequately, might results in
aggressive recurrence. The rate of recurrence accounted for 60.3% of all odontogenic tumors
in Indian population which is significantly high. This case report aims to add to the existing
literature a variation of a clinically appearing dentigerous cyst in a 17 year old female in
maxillary as a case of Mural Unicystic ameloblastoma diagnosed histopathologically.