Abstract
Background: Pulmonary hypoplasia is an uncommon congenital aberration which is often interconnected with other abnormalities.
Objective: To report a rare condition of left pulmonary hypoplasia associated with some great vessels anomalies.
Case Report: A 4-year-old Saudi girl with recurrent chest infections was shown to have left lung hypoplasia along with left sided pulmonary artery agenesis and right sided aortic arch. Her condition improved after medical treatment then she was referred for surgical management.
Conclusions: Lung hypoplasia is a rare disease. However, it should be suspected when children present with recurrent chest infections. Our case had a classical presentation since her infancy period. Early diagnosis of such cases is essential for subsequent management and achieving a good outcome.