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Skeletal involvement in pediatric patients with Gaucher disease and its response to enzyme replacement therapy

Thesis

Last updated: 06 Feb 2023

Subjects

-

Tags

Pediatrics

Advisors

Ragab, Lamis, Yaqout, Khaled, Yusri, Elham

Authors

Abdel-Hamid, Sara Muhammad

Accessioned

2017-04-26 12:42:46

Available

2017-04-26 12:42:46

type

M.Sc. Thesis

Abstract

Gaucher disease is an uncommon autosomal genetic disorder characterized by the deposition of large amounts of lipid, glucosylceramide in the cells of the spleen, liver, and bone marrow. Since treatment is now available, the assessment of skeletal involvement has become important due to its expression. The present work included 22 patients, all of them were subjected to full history, clinical examination. Lab investigations, abdominal sonar, x-ray and MRI of both femurs from hip to knee before and after ERT.

Issued

1 Jan 2004

DOI

http://dx.doi.org/10.21473/iknito-space/33615

Details

Type

Thesis

Created At

28 Jan 2023